Groundbreaking: First-Ever HCC RAF Score Accessible Through REST API
First-Ever HCC RAF Score Accessible Through REST API
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ICD-10-CM Codes D50-D89 D80-D89 D81

ICD-10-CM Diagnosis Code D81

Combined immunodeficiencies

Excludes-1 for D81:

  • autosomal recessive agammaglobulinemia (Swiss type) (D80.0)

Codes Hierarchy:

    • D81  Combined immunodeficiencies
      • D81.0  Severe combined immunodeficiency [SCID] with reticular dysgenesis
      • D81.1  Severe combined immunodeficiency [SCID] with low T- and B-cell numbers
      • D81.2  Severe combined immunodeficiency [SCID] with low or normal B-cell numbers
      • D81.3 Adenosine deaminase [ADA] deficiency
        • D81.30  Adenosine deaminase deficiency, unspecified
        • D81.31  Severe combined immunodeficiency due to adenosine deaminase deficiency
        • D81.32  Adenosine deaminase 2 deficiency
        • D81.39  Other adenosine deaminase deficiency
      • D81.4  Nezelof's syndrome
      • D81.5  Purine nucleoside phosphorylase [PNP] deficiency
      • D81.6  Major histocompatibility complex class I deficiency
      • D81.7  Major histocompatibility complex class II deficiency
      • D81.8 Other combined immunodeficiencies
        • D81.81 Biotin-dependent carboxylase deficiency
          • D81.810  Biotinidase deficiency
          • D81.818  Other biotin-dependent carboxylase deficiency
          • D81.819  Biotin-dependent carboxylase deficiency, unspecified
        • D81.82  Activated Phosphoinositide 3-kinase Delta Syndrome [APDS]
        • D81.89  Other combined immunodeficiencies
      • D81.9  Combined immunodeficiency, unspecified