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ICD-10-CM Diagnosis Code D80.0

Effective Date: 10/01/2015 To 09/30/2025

Hereditary hypogammaglobulinemia

CMS-HCC-V24 CMS-HCC-V28 RxHCC Age Gender Maternity Acute or Chronic MCC
47 115 99 -- -- -- Acute No
Applicable To for D80.0:
  • Autosomal recessive agammaglobulinemia (Swiss type)

  • X-linked agammaglobulinemia [Bruton] (with growth hormone deficiency)

Back-references to D80.0
  • Absence(of) (organ or part) (complete or partial)
    • gamma globulin in blood D80.1
      • hereditary D80.0
    • Agammaglobulinemia(acquired (secondary)) (nonfamilial) D80.1
      • Bruton's X-linked D80.0
        • Swiss type(autosomal recessive) D80.0
          • X-linked(with growth hormone deficiency) (Bruton) D80.0
            • autosomal recessive(Swiss type) D80.0
              • congenital sex-linked D80.0
                • hereditary D80.0
                • Bruton's X-linked agammaglobulinemia D80.0
                • Deficiency, deficient
                  • gammaglobulin in blood D80.1
                    • hereditary D80.0
                  • Hypogammaglobulinemia see also Agammaglobulinemia D80.1
                    • hereditary D80.0
                    • Immunodeficiency D84.9
                      • autosomal recessive, Swiss type D80.0
                      • Syndrome see also Disease
                        • antibody deficiency D80.9
                          • agammaglobulinemic D80.1
                            • hereditary D80.0
                            • congenital D80.0
                              • hypogammaglobulinemic D80.1
                                • hereditary D80.0
                            • Chapter, Section and Diagnosis Prefix for D80.0
                                D50-D89 :

                                Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism

                                D80-D89 :

                                Certain disorders involving the immune mechanism

                                D80 :

                                Immunodeficiency with predominantly antibody defects