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ICD-10-CM Diagnosis Code E78.3

Effective Date: 10/01/2015 To 09/30/2025

Hyperchylomicronemia

CMS-HCC-V24 CMS-HCC-V28 RxHCC Age Gender Maternity Acute or Chronic MCC
-- -- 47 -- -- -- Acute No
Applicable To for E78.3:
  • Chylomicron retention disease

  • Fredrickson's hyperlipoproteinemia, type I or V

  • Hyperlipidemia, group D

  • Mixed hyperglyceridemia

Back-references to E78.3
  • Bürger-Grütz disease or syndrome E78.3
  • Chylomicronemia(fasting) (with hyperprebetalipoproteinemia) E78.3
  • Disease, diseased see also Syndrome
    • Bürger-Grütz(essential familial hyperlipemia) E78.3
      • chylomicron retention E78.3
      • Frederickson's hyperlipoproteinemia, type
        • I and V E78.3
        • Hepatosplenomegaly R16.2
          • hyperlipemic(Bürger-Grütz type) E78.3
          • Hyperchylomicronemia(familial) (primary) E78.3
            • with hyperbetalipoproteinemia E78.3
            • Hyperglyceridemia(endogenous) (essential) (familial) (hereditary) (pure) E78.1
              • mixed E78.3
              • Hyperlipemia, hyperlipidemia E78.5
                • group
                  • D E78.3
                • Hyperlipoproteinemia E78.5
                  • Fredrickson's type
                    • I E78.3
                      • V E78.3
                    • Lipemia see also Hyperlipidemia
                      • retina, retinalis E78.3
                      • Lipidosis E75.6
                        • hepatosplenomegalic E78.3
                        • Prebetalipoproteinemia(acquired) (essential) (familial) (hereditary) (primary) (secondary) E78.1
                          • with chylomicronemia E78.3
                          • Syndrome see also Disease
                            • Bürger-Grütz E78.3
                            • Xanthoma(s), xanthomatosis (primary) (familial) (hereditary) E75.5
                              • with
                                • hyperlipoproteinemia
                                  • Type I E78.3
                                    • Type V E78.3
                                • Related Medications for E78.3
                                  • cholestyramine resin, colestipol, gemfibrozil, lovastatin, fenofibrate, simvastatin, fluvastatin, pravastatin, atorvastatin, colesevelam, rosuvastatin, pitavastatin

                                  Chapter, Section and Diagnosis Prefix for E78.3
                                    E00-E89 :

                                    Endocrine, nutritional and metabolic diseases

                                    E70-E88 :

                                    Metabolic disorders

                                    E78 :

                                    Disorders of lipoprotein metabolism and other lipidemias