Groundbreaking: First-Ever HCC RAF Score Accessible Through REST API
First-Ever HCC RAF Score Accessible Through REST API
Check Now
Image depicting the concept of elevating provider support and enhancing concurrent coding for risk adjustment in healthcare.
Elevate Provider Support:
Enhance Your Concurrent Coding
for Risk Adjustment
Check Now
ICD-10-CM Codes D50-D89 D55-D59 D57

ICD-10-CM Diagnosis Code D57

Sickle-cell disorders

Use Additional for D57:

  • code for any associated fever (R50.81)

Excludes-1 for D57:

  • other hemoglobinopathies (D58.-)

Codes Hierarchy:

    • D57  Sickle-cell disorders
      • D57.0 Hb-SS disease with crisis
        • D57.00  Hb-SS disease with crisis, unspecified
        • D57.01  Hb-SS disease with acute chest syndrome
        • D57.02  Hb-SS disease with splenic sequestration
        • D57.03  Hb-SS disease with cerebral vascular involvement
        • D57.04  Hb-SS disease with dactylitis
        • D57.09  Hb-SS disease with crisis with other specified complication
      • D57.1  Sickle-cell disease without crisis
      • D57.2 Sickle-cell/Hb-C disease
        • D57.20  Sickle-cell/Hb-C disease without crisis
        • D57.21 Sickle-cell/Hb-C disease with crisis
          • D57.211  Sickle-cell/Hb-C disease with acute chest syndrome
          • D57.212  Sickle-cell/Hb-C disease with splenic sequestration
          • D57.213  Sickle-cell/Hb-C disease with cerebral vascular involvement
          • D57.214  Sickle-cell/Hb-C disease with dactylitis
          • D57.218  Sickle-cell/Hb-C disease with crisis with other specified complication
          • D57.219  Sickle-cell/Hb-C disease with crisis, unspecified
      • D57.3  Sickle-cell trait
      • D57.4 Sickle-cell thalassemia
        • D57.40  Sickle-cell thalassemia without crisis
        • D57.41 Sickle-cell thalassemia, unspecified, with crisis
          • D57.411  Sickle-cell thalassemia, unspecified, with acute chest syndrome
          • D57.412  Sickle-cell thalassemia, unspecified, with splenic sequestration
          • D57.413  Sickle-cell thalassemia, unspecified, with cerebral vascular involvement
          • D57.414  Sickle-cell thalassemia, unspecified, with dactylitis
          • D57.418  Sickle-cell thalassemia, unspecified, with crisis with other specified complication
          • D57.419  Sickle-cell thalassemia, unspecified, with crisis
        • D57.42  Sickle-cell thalassemia beta zero without crisis
        • D57.43 Sickle-cell thalassemia beta zero with crisis
          • D57.431  Sickle-cell thalassemia beta zero with acute chest syndrome
          • D57.432  Sickle-cell thalassemia beta zero with splenic sequestration
          • D57.433  Sickle-cell thalassemia beta zero with cerebral vascular involvement
          • D57.434  Sickle-cell thalassemia beta zero with dactylitis
          • D57.438  Sickle-cell thalassemia beta zero with crisis with other specified complication
          • D57.439  Sickle-cell thalassemia beta zero with crisis, unspecified
        • D57.44  Sickle-cell thalassemia beta plus without crisis
        • D57.45 Sickle-cell thalassemia beta plus with crisis
          • D57.451  Sickle-cell thalassemia beta plus with acute chest syndrome
          • D57.452  Sickle-cell thalassemia beta plus with splenic sequestration
          • D57.453  Sickle-cell thalassemia beta plus with cerebral vascular involvement
          • D57.454  Sickle-cell thalassemia beta plus with dactylitis
          • D57.458  Sickle-cell thalassemia beta plus with crisis with other specified complication
          • D57.459  Sickle-cell thalassemia beta plus with crisis, unspecified
      • D57.8 Other sickle-cell disorders
        • D57.80  Other sickle-cell disorders without crisis
        • D57.81 Other sickle-cell disorders with crisis
          • D57.811  Other sickle-cell disorders with acute chest syndrome
          • D57.812  Other sickle-cell disorders with splenic sequestration
          • D57.813  Other sickle-cell disorders with cerebral vascular involvement
          • D57.814  Other sickle-cell disorders with dactylitis
          • D57.818  Other sickle-cell disorders with crisis with other specified complication
          • D57.819  Other sickle-cell disorders with crisis, unspecified